Logo do repositório
 
Publicação

Cardiac rehabilitation in a transplanted person with emery-dreifuss muscular dystrophy

dc.contributor.authorLoureiro, Maria
dc.contributor.authorBranco, Carlos
dc.contributor.authorDuarte, João
dc.contributor.authorCoutinho, Gonçalo
dc.contributor.authorMartins, Maria Manuela
dc.contributor.authorNovo, André
dc.date.accessioned2023-07-06T14:28:18Z
dc.date.available2023-07-06T14:28:18Z
dc.date.issued2023
dc.description.abstractEmery-Dreifuss muscular dystrophy is a rare hereditary neuromuscular disease. Its manifestations begin primarily in childhood. The most frequent manifestations are progressive muscle weakness, atrophy that usually begins in the scapulavertebral region, extending later to the pelvic girdle, and spinal stiffness. Patients can also manifest cardiac involvement as palpitations, syncope, exercise intolerance, congestive heart failure, and variable heart rhythm disturbances The presence and severity of these manifestations can vary according to the individual and the disease’s subtypes.Cardiac involvement is the most worrisome feature of this disease, and there are some reports of the need for heart transplantation in this dystrophy.pt_PT
dc.description.versioninfo:eu-repo/semantics/publishedVersionpt_PT
dc.identifier.citationLoureiro, Maria; Branco, Carlos ; Duarte, João; Coutinho, GF ; Martins, MM; Novo, André (2023). Cardiac rehabilitation in a transplanted person with emery-dreifuss muscular dystrophy. Arquivos Brasileiros de Cardiologia. ISSN 0066-782X. 120:7, p. 1-3pt_PT
dc.identifier.doi10.36660/abc.20220560pt_PT
dc.identifier.issn0066-782X
dc.identifier.urihttp://hdl.handle.net/10198/28510
dc.language.isoengpt_PT
dc.peerreviewedyespt_PT
dc.publisherSociedade Brasileira de Cardiologiapt_PT
dc.rights.urihttp://creativecommons.org/licenses/by/4.0/pt_PT
dc.subjectHeart transplantpt_PT
dc.subjectEmery-dreifuss muscular dystrophypt_PT
dc.subjectCardiac rehabilitationpt_PT
dc.titleCardiac rehabilitation in a transplanted person with emery-dreifuss muscular dystrophypt_PT
dc.typejournal article
dspace.entity.typePublication
oaire.citation.endPage3pt_PT
oaire.citation.issue7pt_PT
oaire.citation.startPage1pt_PT
oaire.citation.titleArquivos Brasileiros de Cardiologiapt_PT
oaire.citation.volume120pt_PT
person.familyNameNovo
person.givenNameAndré
person.identifierH-1386-2012
person.identifier.ciencia-id7D14-8584-AB2B
person.identifier.orcid0000-0001-8583-0406
person.identifier.scopus-author-id612710
rcaap.rightsopenAccesspt_PT
rcaap.typearticlept_PT
relation.isAuthorOfPublicationf17cfa22-2a97-4396-bdc6-4570baee6885
relation.isAuthorOfPublication.latestForDiscoveryf17cfa22-2a97-4396-bdc6-4570baee6885

Ficheiros

Principais
A mostrar 1 - 1 de 1
Miniatura indisponível
Nome:
0066-782X-abc-120-07-e20220560-en.x55156.pdf
Tamanho:
199.09 KB
Formato:
Adobe Portable Document Format
Licença
A mostrar 1 - 1 de 1
Miniatura indisponível
Nome:
license.txt
Tamanho:
1.75 KB
Formato:
Item-specific license agreed upon to submission
Descrição: